|Types||Percentage of occurrence||Morphology||Histopathology||Association|
|0||1–3%||Solid appearance with small and firm lungs||Tracheobronchial origin. Microscopically shows bronchiolar type airway with cartilage, smooth muscle, and glands separated by abundant mesenchymal tissue.||Differential diagnosis: bronchogenic cyst|
|1||50–70%||Single or multiple large cysts (> 2 cm)||Wall contains flattened, cuboidal cells. It also contains prominent smooth muscle and elastic tissue. Sometime mucus producing cells are seen and presence of cartilage is very rare||Contralateral mediastinal shift|
|2||15–30%||Multiple small cysts (< 2 cm)||Cyst wall lined by ciliated cuboidal to columnar epithelium that resembles respiratory bronchioles. Distended alveoli are present between the epithelium lined cyst. Mucus cells and cartilage are not seen.||Systemic anomalies like Bilateral renal agenesis, abdominal wall defects, hydrocephalus, spinal deformities, diaphragmatic hernia, jejunal atersia, tracheoesophageal fistula, imperforate anus, ventriculoseptal defects, tetralogy of Fallot, truncus arteriosis, and sirenomelia|
|3||5–10%||Bulky non-cystic lesions||Bronchial-like structures are lined by ciliated cuboidal epithelium and separated by masses of alveolus-sized structures by non-ciliated cuboidal epithelium .||
Contralateral mediastinal shift.|
Rarely associated with esophageal cyst.
|4||10–15%||Distal acinar origin. Large cysts (> 10 cm) lined by flattened epithelium and resting on loose mesenchymal tissue||Differential diagnosis: pulmonary blastoma|