Fig. 3

MRI pelvis of a 14-year-old female with primary amenorrhea and cyclic lower abdominal pain. Axial T1W SE image (a) reveals a small rudimentary uterus in right hemipelvis, with hyperintense contents (white arrowhead) within the endometrial cavity and a large dilated right fallopian tube with hyperintense contents (black arrow). Mid-sagittal T2W SE sequence (b) depicts shading within the rudimentary horn and tube, with non-visualization of cervix and vagina. Axial T1 FS (c) shows no suppression of T1 hyperintense contents, confirming hematometra and hematosalpinx. Axial T2*GRE (d) shows hemosiderin lining of the hematosalpinx (curved arrow) and dependent blooming foci in the rudimentary horn. Cervix and vagina were not visualized on MRI, suggesting their aplasia. Right ovary (e) and left ovary (f) (white arrows) are normal. Features are consistent with Mayer-Rokitansky-Küster-Hauser syndrome with functional rudimentary right horn with hematometra, right hematosalpinx, and aplastic cervix and vagina